cardiotomskСибирский журнал клинической и экспериментальной медициныSiberian Journal of Clinical and Experimental Medicine2713-29272713-265XTSU publishing10.29001/2073-8552-2022-37-3-65-74cardiotomsk-1504Research ArticleОБЗОРЫ И ЛЕКЦИИREVIEWS AND LECTURESПервичные кардиомиопатии в детском возрасте: клинические и диагностические особенности (обзор литературы)Primary cardiomyopathies in childhood: clinical and diagnostic features (literature review)https://orcid.org/0000-0003-4823-4378ПлотниковаИ. В.PlotnikovaI. V.

Плотникова Ирина Владимировна, д-р мед. наук, заведующий отделением детской кардиологии

634012, Томск, ул. Киевская, 111а

Irina V. Plotnikova, Dr. Sci. (Med.), Head of the Department of Pediatric Cardiology

111a, Kievskaya str., Tomsk, 634012

ivp@cardio-tomsk.ruhttps://orcid.org/0000-0002-2056-4060СвинцоваЛ. И.SvintsovaL. I.

Свинцова Лилия Ивановна, д-р мед. наук, ведущий научный сотрудник, отделение детской кардиологии

634012, Томск, ул. Киевская, 111а

Liliya I. Svintsova, Dr. Sci. (Med.), Leading Research Scientist, Department of Pediatric Cardiology

111a, Kievskaya str., Tomsk, 634012

lis@cardio-tomsk.ruhttps://orcid.org/0000-0002-3947-4903ДжаффароваО. Ю.DzhaffarovaO. Yu.

Джаффарова Ольга Юрьевна, канд. мед. наук, старший научный сотрудник, отделение детской кардиологии

634012, Томск, ул. Киевская, 111а

Olga Yu. Dzhaffarova, Cand. Sci. (Med.), Senior Research Scientist, Department of Pediatric Cardiology

111a, Kievskaya str., Tomsk, 634012

oyd@cardio-tomsk.ruhttps://orcid.org/0000-0003-2469-8098КартофелеваЕ. О.KartofelevaE. O.

Картофелева Елена Олеговна, младший научный сотрудник, отделение детской кардиологии

634012, Томск, ул. Киевская, 111а

Elena O. Kartofeleva, Junior Research Scientist, Department of Pediatric Cardiology

111a, Kievskaya str., Tomsk, 634012

lenakartofeleva@yandex.ruhttps://orcid.org/0000-0002-5352-1323ПеревозниковаЮ. Е.PerevoznikovaYu. E.

Перевозникова Юляна Евгеньевна, младший научный сотрудник, отделение детской кардиологии

634012, Томск, ул. Киевская, 111а

Yulyana E. Perevoznikova, Junior Research Scientist, Department of Pediatric Cardiology

111a, Kievskaya str., Tomsk, 634012

muser-yuliana@yandex.ruhttps://orcid.org/0000-0002-3081-9477ПавлюковаЕ. Н.PavlyukovaE. N.

Павлюкова Елена Николаевна, д-р мед. наук, профессор, заведующий отделением атеросклероза и хронической ишемической болезни сердца

634012, Томск, ул. Киевская, 111а

Elena N. Pavlyukova, Head of the Department of Atherosclerosis and Coronary Artery Disease

111a, Kievskaya str., Tomsk, 634012

pavluk@cardio-tomsk.ruНаучно-исследовательский институт кардиологии, Томский национальный исследовательский медицинский центр Российской академии наукРоссияCardiology Research Institute, Tomsk National Research Medical Center, Russian Academy of SciencesRussian Federation2022201020223736574Copyright © Плотникова И.В., Свинцова Л.И., Джаффарова О.Ю., Картофелева Е.О., Перевозникова Ю.Е., Павлюкова Е.Н., 20222022Плотникова И.В., Свинцова Л.И., Джаффарова О.Ю., Картофелева Е.О., Перевозникова Ю.Е., Павлюкова Е.Н.Plotnikova I.V., Svintsova L.I., Dzhaffarova O.Y., Kartofeleva E.O., Perevoznikova Y.E., Pavlyukova E.N.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.sibjcem.ru/jour/article/view/1504

Первичные кардиомиопатии в детском возрасте представляют собой редкое, но серьезное заболевание, которое является частой причиной сердечной недостаточности и наиболее частой причиной трансплантации сердца у детей старше 1 года. За последние десятилетия диагностика кардиомиопатии продвинулась от традиционных клинических подходов к новым генетическим и визуализационным методам. В статье представлен обзор литературных данных о современной классификации первичных педиатрических кардиомиопатий, особенностях клинического течения и визуализации, которая является неотъемлемой частью диагностики на основе первичного морфофункционального фенотипа.

Primary cardiomyopathies in childhood are a rare but serious disease that is a common cause of heart failure and the most common reason for heart transplantation in children over one year of age. Over the past decades, the diagnosis of cardiomyopathy has advanced from traditional clinical imaging methods to new genetic and imaging techniques. The article presents a review of the literature data on the modern classification of primary pediatric cardiomyopathies and the features of the clinical course and imaging, which is an integral part of the diagnosis based on the primary morphofunctional phenotype.

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The authors declare that there are no conflicts of interest present.