ISOLATED LEFT VENTRICULAR APICAL HYPOPLASIA, RARE INBORN CARDIOMYOPATHY
https://doi.org/10.29001/2073-8552-2018-33-1-21-26
Abstract
The review of data of literature concerning the description of clinical cases of isolated left ventricular apical hypoplasia (LVAH) in 42 patients are presented. left ventricular apical hypoplasia is characterized by 1) a spherical left ventricular with a cut-off tip and a swelling of the interventricular septum to the right in combination with systolic dysfunction of left ventricular; 2) replacement of the myocardium of the upper limb with fat tissue; 3) localization of papillary muscles on the flattened apex of the left ventricular; 4) elongated right ventricle (RV), flowing around the top of the upper left vertex. The course of this condition may be asymptomatic, or manifest as a clinic of biventricular heart failure with high pulmonary hypertension and heart rhythm disturbances.
About the Authors
V. I. Skidan
Federal Center for Cardiovascular Surgery
Russian Federation
Russian Federation
Cand. Sci. (Med.), Physician of Functional Diagnostics Department
2в, Krasnodarskaya str., Khabarovsk, 680009
E. N. Pavlyukova
Cardiology Research Institute, Tomsk National Research Medical Center, Russian Academy of Sciences
Russian Federation
Russian Federation
Dr. Sci. (Med.), Leading Research Worker of atherosclerosis and chronic ischemic heart disease department
111а, Kievskaya str., Тоmsk, 634012
G. P. Narcissova
Meshalkin Siberian Federal Biomedical Research Center
Russian Federation
Russian Federation
Dr. Sci. (Med.), Functional Diagnostician of diagnostic center No. 1, Leading Research Worker, Group of functional and ultrasonic diagnostics of Center of New Technologies
15, Rechkunovskaya str., Novosibirsk, 630055
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Review
For citations:
Skidan V.I., Pavlyukova E.N., Narcissova G.P. ISOLATED LEFT VENTRICULAR APICAL HYPOPLASIA, RARE INBORN CARDIOMYOPATHY. Siberian Journal of Clinical and Experimental Medicine. 2018;33(1):21-26. (In Russ.) https://doi.org/10.29001/2073-8552-2018-33-1-21-26
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